Pdf extralobar pulmonary sequestration with combined. A pulmonary sequestration is a medical condition wherein a piece of tissue that ultimately develops into lung tissue is not attached to the pulmonary arterial blood supply, as is the case in normally developing lung. Intralobar pulmonary sequestration is located within the visceral pleura and is surrounded by normal lung, whereas extralobar pulmonary sequestration is separated from the lung by a pleural envelope. Extralobar sequestration is in conformity with a true accessory lung, with its own pleural envelope and accounts for 15%25% of all pulmonary sequestrations. Lobulillo pulmonar secundario by prezi user on prezi. Extrathoracic intradiaphragmatic extralobar pulmonary sequestrations are an extremely rare subset of bronchopulmonary sequestrations and there have been very few reported cases until now.
Extralobar pulmonary sequestration is a rare congenital in order to allow the paresis of the phrenic nerve to be. Anomalous pulmonary artery from the aorta associated with. Unilateral coexisting intralobar and extralobar pulmonary sequestrations. This pdf is available for free download from a site hosted by medknow publications. Herein, we report a rare case of yearold girl who presented with abdominal pain and fever was diagnosed as infarction of torsed extralobar pulmonary. Pulmonary sequestration is a nonfunctioning lung mass with an abnormal connection to tracheobronchial trees and an anomalous systemic artery supply. Extralobar sequestration, elective resection, asymptomatic malformation. Bilateral sequestrations were rareonly three cases had been reported. It is the commoner type of pulmonary sequestration four times commoner than extralobar sequestration, accounting for 75% of all sequestrations and is characterized by the sequestration surrounded by normal lung tissue without its own pleural covering. Read upper thoracic extralobar pulmonary sequestration with anomalous blood supply from the subclavian artery, journal of pediatric surgery on deepdyve, the largest online rental service for scholarly research with thousands of academic publications available at your fingertips. Intradiaphragmatic extralobar pulmonary sequestration in. Endovascular treatment of pulmonary sequestration with. In the same patient, extralobar pulmonary sequestration was detected and resected. Survival of chinese patients with pulmonary arterial.
Extralobar sequestration of lung in newborn infant. Bronchopulmonary sequestration is the term given to a region of lung parenchyma that is partially or completely. Extralobar pulmonary sequestration mimicking an adrenal. Infarction of torsed extralobar pulmonary sequestration in. Els receives vascular supply mainly from the aorta thoracic or abdominal or from other arterial vessels splenic, subclavian, gastric, intercostal or. While the diagnosis of es can be done in 60% of the cases in the first decade of life this could be achieved for only half of the patients with is cases.
This article is from journal of cardiothoracic surgery, volume 9. Unique extralobar sequestration with atypical location and. The radiological and pathological findings of lung sequestration in a premature infant are described. Videoassisted thoracoscopic surgery revealed the mass to be a rare case of extralobar pulmonary sequestration that had undergone infarction. The anomaly causes a predisposition for pulmonary complications such as infection and hemoptysis. Pulmonary sequestration is a rare congenital pulmonary disorder defined as an area of dysplastic and nonfunctioning pulmonary tissue with an anomalous systemic blood supply. Extralobar diaphragmatic sequestration of the lung. Pulmonary sequestration intralobar radiology reference. Edward araujo junior,1,2 and sebastiao marques zanforlin filho1. Imaging of extralobar pulmonary sequestration in a patient. The mass was identified to be an extralobar pulmonary sequestration. A case report, journal of pediatric surgery on deepdyve, the largest online rental service for scholarly research with thousands of academic publications available at your fingertips. Lectura sistematica by diego torres cardenas on prezi. Pulmonary sequestration is an uncommon congenital condition for which surgical resection is usually.
Abstractextralobar pulmonary sequestrations may be located in intrathoracic or extrathoracic. However, during pulmonary resection, inadvertent injury of the aberrant artery can cause a lifethreatening hemorrhage. In a previous study of chinese patients with idiopathic pulmonary arterial hypertension ipah in the nontargeted therapy era, we reported 1 and 3year survival. There are two types of sequestrations, intralobar and extralobar. If so, share your ppt presentation slides online with. Our institution has no clear policy, therefore both therapies are performed. Although there are numerous reports in the literature by surgeons who have encountered anomalous arteries arising from either. Els is covered by its own pleura and this is what differentiates els from ils. Uniportal thoracoscopic lobectomy for intralobar pulmonary. If you continue browsing the site, you agree to the use of cookies on this website. Author links open overlay panel toshihiro osaki md a mantaro. It is typically classified into intralobar and extralobar sequestration. Pulmonary sequestration is a congenital syndrome characterized by abnormal systemic blood supply to the lung, usually the lower lobe. Seven cases proved by surgical resection and subsequent pathologic examination form the basis of the study.
The sequestered lung was completely excised using a videoassisted thoracoscopic approach. Secondary diaphragmatic eventration after resection of. The patient is symptom free at 41 months after this secondary procedure. Pulmonary sequestration is a congenital malformation representing an area of nonfunctional pulmonary tissue, not communicating with the bronchial tree and supplied by one or more systemic arteries. The noun sequestrum has wellknown orthopedic connotations and is defined in stedmans medical dictionary as a piece of necrosed bone which has become separated from the surrounding healthy osseous tissue. Secuestro pulmonar extralobar asociado a malformacion. This sequestered tissue is therefore not connected to the normal bronchial airway architecture, and fails to function in, and contribute to, respiration of the organism. The ideal treatment strategy for pulmonary sequestration whether resection or embolization in childhood is not clearly defined. Read imaging of extralobar pulmonary sequestration in a patient with tetralogy of fallot with pulmonary atresia, ventricular septal defect and multiple aorto.
Pulmonary sequestration ps is a rare congenital malformation of the lower respiratory tract, and the standard treatment of the disease has been conventional surgery with resection of abnormal parenchyma. Infarcted pulmonary sequestration of either type has not been described previously. Pulmonary sequestration is a rare congenital present from birth malformation where nonfunctioning lung tissue is separated from the rest of the lung and supplied with blood from an unusual source, often an artery from systemic circulation. Sihoe, qigang luo, guangqiang shao, yue li, jinglong li and dazhi pang abstract background. Several es cases existing in the right and left hemithorax upper zones are cited in the literature. Extralobar pulmonary sequestration is the less common type of pulmonary sequestration, accounting only for 1525%. A computed tomography scan of the abdomen was negative, but a pleural effusion and mass was noted in the lower left thorax. Stem cell therapy for idiopathic pulmonary fibrosis. Pulmonary sequestrations may be defined as intralobular or extralobular, depending on their location. Excel individual calculator a version of the desktop software has been developed as an excel macro excel sheet calculator this runs gli calculations on an excel database. Extralobar pulmonary sequestrations may be located in intrathoracic or extrathoracic areas. Coil occlusion of aberrant arteries to pulmonary sequestration in a case with pulmonary atresia with intact ventricular septum. Endovascular treatment of pulmonary sequestration in.
Pdf treatment strategies for pulmonary sequestration in. Semiologia radiologica basica pulmonar patron alveolar ocupacion del espacio aereo pulmonar sangre, pus, agua, cel. Unilateral coexisting intralobar and extralobar pulmonar y sequestrations. Prenatal diagnosis of fetal intraabdominal extralobar.
Intradiaphragmatic extralobar pulmonary sequestration in adult. Torsion of pulmonary extralobar sequestration is extremely rare in childhood and adolescence, and as it presents with a variety of symptoms ranging from intermittent pain to fever from infarction, differential diagnosis is necessary. Pulmonary sequestrations were divided into two types, intralobar sequestration 83. Bronchopulmonary sequestration presenting as a spontaneous. We report a unique extralobar pulmonary sequestration in the upper thoracic region with 3 aberrant. Lactante vomitador estenosis hipertrofica del piloro is the property of its rightful owner. We report a unique extralobar pulmonary sequestration in the upper thoracic region with 3 aberrant vessels connecting to the right subclavian artery, right superior pulmonary vein, and right pulmonary artery in a 20yearold man.
Abstract a 4yearold male presented with abdominal pain. Abstracta laparoscopic transperitoneal approach allowed for. Prenatal diagnosis of fetal intraabdominal extralobar pulmonary sequestration. Pulmonary sequestration is an uncommon congenital condition for which surgical resection is usually indicated either via open thoracotomy or conventional multiport videoassisted thoracoscopic surgery vats. Pulmonary sequestration extralobar radiology reference. Thoracoscopic resection of intra and extralobar pulmonary. Extralobar sequestration of pulmonary tissues is relatively rare and seldom produces symptoms. Although sequestrations are asymptomatic, they may become symptomatic by events such as infection, degeneration and trauma. Mar 11, 2014 este video versa sobre hdc patitas cortas. The lesion typically manifests in the newborn period or early infancy with symptoms of respiratory distress. Read prenatal diagnosis of an extralobar pulmonary sequestration, archives of gynecology and obstetrics on deepdyve, the largest online rental service for scholarly research with thousands of academic publications available at your fingertips. Extralobar sequestration is a rare congenital anomaly that consists of pulmonary tissue anatomically separate from normal lung and usually deriving its blood supply from systemic vessels.
Unilateral coexisting intralobar and extralobar pulmonary. There was a leftsided variant of the extralobar type with double systemic arterial blood supply, single systemic venous drainage, and an incomplete bronchial tree for. Infarction of an extralobar pulmonary sequestration in a. Diagnosis of intraabdominal extralobar pulmonary sequestration by means of ultrasound in a neonate. This discussion is concerned with the roentgen diagnosis of an anomalous systemic artery to the lung associated with congenital cystic pulmonary abnormalities. It is usually encountered in infants, most being diagnosed before six months. Bronchopulmonary sequestration is a relatively rare medical condition wherein a mass of nonfunctioning primitive lung tissue does not communicate with the tracheobronchial tree and receives its blood supply from an anomalous systemic artery. The sequestration of pulmonary tissue has been defined by potter1 to be masses of pulmonary tissue which have no communication with the bronchial tree. Surgical resection is the standard of care for both intralobar and extralobar pulmonary sequestration. Patients usually present before the third decade with recurrent infection. Pulmonary sequestration is a congenital anomaly resulting in nonfunctioning pulmonary tissue with no.
Although extralobar pulmonary sequestration eps is a rare congenital lung anomaly, it is the second most common lung malformation in children, accounting for 0. Thoracoscopic resection of intra and extralobar pulmonary sequestration in the first 3 months of life. Case report open access uniportal thoracoscopic lobectomy for intralobar pulmonary sequestration alan d. Unique extralobar sequestration with atypical location and aberrant vessels. The patient continued to do well and remained pneumonia free. Of the two types of sequestration, intralobar sequestration is technically more challenging to resect. Upper thoracic extralobar pulmonary sequestration with. This is a report of a patient with an infarcted extralobar pulmonary sequestration, an unusual complication of an uncommon entity. Journal of the society of laparoendoscopic surgeons, volume 16. The finding of an accessory lung can alert the astute. Extralobar lung sequestration associated with fatal. It accounts for a small portion of pulmonary malformations 1,2. Two forms of pulmonary sequestration are described, intralobar and extralobar.
Secuestro pulmonar extralobar asociado a malformacion adenomatoide quistica tipo 2 1. There are two subtypes of pulmonary sequestration, namely intralobar sequestration ils and extralobar sequestration els. Read preoperative diagnosis of extralobar pulmonary sequestration with unusual vasculature. Extralobar sequestration of lung in newborn infant jama.
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